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简介：AbstractIntroduction:Glucose transporter type 1 (Glut1) deficiency syndrome is a treatable neurometabolic disorder characterized by seizures, developmental delay, and hypoglycorrhachia. Due to the rareness and non-specific clinical manifestations, it is usually mis- or underdiagnosed.Case presentation:We report the case of a toddler who presented with afebrile epileptic seizures and abnormal gait. Brain imaging and electroencephalogram were normal. Further investigation of the cerebrospinal fluid revealed hypoglycorrhachia that was the clue to the diagnosis of Glut1 deficiency syndrome and the initiation of treatment with ketogenic diet.Conclusion:Our case highlights the importance of lumbar puncture while investigating a child with epileptic seizures and abnormal gait or developmental delay, in order not to miss treatable neurometabolic conditions, such as Glut1 deficiency syndrome.

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简介：台风玛吉(1999)与另一个热带气旋系统交往了并且沿着在它的预先登陆的阶段期间是有点反常的一条西南西轨道移动了。Twonumerical实验在这篇论文被执行用有一个热带气旋bogusing计划的数字天气预言模型系统由沿海、大气的研究的中心开发了的中央规模在台风玛吉的轨道上学习相互作用的效果，科技的香港大学。结果表演气旋系统交往的withMaggie是为玛吉的反常磁道的主要因素。

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简介：Thispaperdealswithanimportantsubjectofrejectingtheabnormaldataintelligentlyinthedynamicdatasystem.Basedontheprincipleofnearestneighboroffuz-zymathematics,anapproachofmathematicallyabstractingthehumanthinkingandphys-icalpracticeknowledgeisdiscussed,anewmethodofautomaticrejectionofabnormalda-taisthenproposed.Theexperimentalresultsshowthatthemethodisavailabletothepractice.

简介：Thegrain-growthbehaviorofAl2O3powdercompactswithsmallcontents(<5wt%)ofvariousdopantswasstudied.Theexistenceoftabularsub-grainswereobservedwithallthefollowingdopants:V2O5,MgO+Y2O3andNa2B4O7+V2O3+Pr.Thetabularsubgrainsaredefinedastheabnormalgrainslongerthan30μmwithanaspectratio>50.Theycanbeobservedwhenthesinteringtemperaturearehigherthan1850℃。

简介：Thenoisedatainverticalcomponentrecordsof85seismicstationsinFujianProvinceduring2012isusedastheresearchobjectinthispaper.Thenoisedataisdividedintofiveminutesegmentstocalculatethepowerspectra.Thehighreferencelineandlowreferencelineofstationarethenidentifiedbydrawingaprobabilitydensityfunctiongraph(PDF)usingthepowerspectralprobabilitydensityfunction.Moreover,accordingtotheanomaliesofPDFgraphsin85seismicstations,theabnormalnoiseisdividedintofourcategories:droppedpacket,lownoise,highnoise,andmediannoiseanomalies.Afterwards,fourselectionmethodsarefoundbythehighorlownoisereferencelineofthestations,andthesystemofreal-timemonitoringofseismicnoiseisformedbycombiningthefourselectionmethods.Noiserecordsof85seismicstationsinFujianProvinceinJuly2013areselectedforverification,andtheresultsshowthattheanomalousnoise-recognitionsystemcouldreacha90%successrateatmoststationsandtheeffectofselectionareverygood.Therefore,itcouldbeappliedtotheseismicnoisereal-timemonitoringinstations.

简介：柏油的具体核心(ACC)水坝广泛地在中国被造。许多ACC水坝执行井，而是其它在此处学习的西方的中国包括盒子经历了重要的漏。浸透不饱和的水流动的一个数字模特儿被适应通过水坝模仿渗出物。由在不同条件下面比较正常、反常的渗出物地，为实际反常渗出物地的主要原因被识别并且在转变地区(TZ)和下游的水坝壳在ACC和非计划中的、低渗透层(LPL)归因于一个缺点。这些结论与水坝的状况和表演一致。不适当的ACC构造过程可能在ACC引起了缺点。ACC厚度的一个突然的变化可能导致了压力集中并且引起了ACC失败。为TZ和水坝壳的材料来源从说明，和土壤阶段复杂、变化因为TZ不充分地被控制。特别地，测试证明渗透在水坝的这二部分在大范围上变化。意外LPL可能在两个区域存在，并且连续地延长。

简介：Basedontheexperimentalresultsofabnormalinfraredeffects(AIREs)formoleculesadsorbedontransition-metalnanostructuredsurfaces,theinteractionsandthepolarizabilityoftheadsorbedmoleculesareanalyzedtheoretically.Bynumericalsimulations,thenormalabsorptionspectrum,theFano-likebipolarspectrumandtheanti-absorptionspectrumoftheadsorbedCOmoleculesareobtainedrespectively.Theresultsshowthattheadsorbedmoleculesonametalnanostructuredsurfacecanaccumulatetogetherduestotheeffectoflocalexternalelectricfield,whichleadstoachangeinimaginarypartofthemolecularpolarizabilitywithinacertainrangeoffrequency,andevenanegativevaluemayappear.

简介：Adoublemutantwithstreakedleafandabnormalfloretwasfoundandtemporarilynamedstreakedleafandfloralorgannumbermutant(st-fon).Forthismutant,besideswhitestreakappearedonculm,leavesandpanicles,thenumberoffloralorgansincreasedandfloretscracked.Theextremephenotypewasthatseveralsmallfloretsgrewfromonefloretorbranchrachisinsmallfloretsextendedanddevelopedintopanicles.Byusingtransmissionelectronmicroscopetoobservetheultrastructureofwhitehistocytesofleavesattheseedlingstage,thewhitetissueswhichshowedabnormalplastids,lamellasandthylakoidscouldnotdevelopintonormalchloroplast,andthedevelopmentofchloroplastwasblockedattheearlygrowthstageofplastid.Scanningelectronmicroscopeandparaffinsectionwerealsousedtoobservethedevelopmentoffloralorgans,andtheresultsindicatedthatthedevelopmentoffloralmeristemwasoutoforderandunlimited,whereasinthetwistyleaves,vascularbundlesheathcellsgrewexcessively,orsomebubblycellsincreased.Geneticanalysescarriedoutbymeansofcrossandbackcrosswithfournormal-leaf-colormaterialsrevealedthatthemutantisofcytoplasminheritance.

简介：ByemployingtheimprovedT42L9spectralmodelintroducedbyNMC(Beijing)fromECMWFandutilizingtheFGGE-IIIbdatacoveringtheperiodof14—19June1979,theatmosphericresponsestotheabnormalsoilmoistureduringthemedium-rangeperiodhavebeenstudiednumerically.Accordingtotheinitialfieldat12GMT14June,afive-daynumericalexperimentunderdifferentconditionsofthesoilmoisturehasbeencarriedoutrespectively.ThemonthlymeanclimatologicalsoilmoistureforJunehasbeenusedinthecontrolexperimentintheinitialtimeanditchangeswithtimeaccordingtothemoisturebudgetequationatthelandsurface.Comparingwiththeexperimentswithdryorwetsoil.onecanconcludethat:1)Sourceofprecipitationovercontinentsinsummerconsistsoftheland-surfaceevaporationandthemoisturetransferfromoceans.Theirintensitiesarecomparableduringthemedium-rangetimescalewhenthesoilevaporatesitsmoisturesufficiently.Therefore,thesoilmoisturecaninfluencetheglobalprecipitationandthegeneralcirculationsignificantly;2)Byinfluencingthethermodynamicdifferencebetweenlandandsea,thesoilmoisturecanchangetheintensityofmonsoonandprecipitationdistribution;3)Theresponseoftheatmospheretotheabnormalsoilmoisturehasthecharacteristicsofgeographicaldistributionandnonlinearinteractions;4)Humanactivi-tiesontheworldcaninfluencetheenvironmentgreatly.

简介：Inthispaper,byvirtueofthecombinatorialoptimizationandgrouptestingmethodand,withascalewithoutweight,wedetectncoinscontainingatmostoneabnormal.Thencoinsareindistinguishableonlybytheirappearances.Wederiveanoptimalprocedureofdeterminingwhetherallthenballsarenormalornotandinthelattercase,ourprocedure(algorithm)alsotellswhethertheabnormalweighsmoreorweighslessthaneachofthenormals.Theoptimalalgorithmobtainedinthispaperisconstructive.

简介：AquantitativediagnosisiscarriedoutfortheupwardbranchofalocalmeridionalcirculationoversouthernChina(SC)duringtheabnormalsnowstormswithseverefreezingrainfrom10Januaryto3February2008.Thediagnosticstudyshowsthattheupwardbranchismainlyassociatedwiththezonaladvectionofwesterlymomentumandmeridionaltemperatureadvectioninsteadofthelatentheating(whichiscommonlythedominantfactorinmanyotherstormcases).Thecorrespondingweatheranalysesindicatethat(1)thezonaladvectionofwesterlymomentumrepresentstheeffectoftheupper-leveldivergenceontheanticyclone-shearsideintheentranceofa200hPawesterlyjetwithawestwarddeviationfromitsclimatologicallocationoversouthwesternJapan;(2)themeridionaltemperatureadvectionrepresentstheinteractionbetweenthemid-lowerlayer(850to400hPa)warmadvectionoverSC(aheadoftemperatureandpressuretroughswiththelattertroughdeeperthantheformerintheBayofBengal)andcoldadvectionovernorthChina(steeredbyanunderlyingflowat500hPa);(3)therelativelyweakvaportransport(comparedtothatofspring,summerandautumn)fromtheBayofBengalandtheSouthChinaSeatoSCandtheexistenceofatemperatureinversionlayerinthelowertroposphereoverSCdiminishtheeffectoflatentheating.Withthesignificantincreaseofvaportransportafter24January,theroleoflatentheatingisupgradedtobecomethethirdpositivecontributortotheupwardbranchoverSC.

简介：ＴｈｅｓｙｎｔｈｅｔｉｃａｌｅｌａｓｔｉｃｃｈａｒａｃｔｅｒｉｓｔｉｃｐａｒａｍｅｔｅｒｓｏｆｅａｒｔｈｔｉｄｅａｎｄｉｔｓａｂｎｏｒｍａｌｐｒｅｃｕｒｓｏｒｅｖｏｌｕｔｉｏｎＹＡＮ－ＢＩＮＺＨＡＮＧ（张雁滨）ＪＵＮＪＩＡＮＧ（蒋骏）ＸＵ－ＤＯＮＧＬ...

简介：基于性质，构造和Huatugou油的反常压力系统的分发在Qaidam回答的核心样品，很好严峻的数据，和水库液体的全面学习盆被讨论。在压力系统和烃累积之间的关联被分析相应液体特征探讨。结果证明整个的Huatugou油领域有低形成压力和低液体精力；因此，烃是难的移居，它便于形成主要水库。学习水库，在Xiayoushashan形成定位了(N21)和Shangganchaigou形成(N1)是相对浅的并且有中等的孔和低渗透。他们分别地是有0.61和0.72的一个平均形成压力系数的反常低压的水库。根据压力系数和地热的异例，N1和N21形成属于二个独立温度压力系统，和前者有稍微更高的精力。低压的分隔空间作为主要身体由远侧的工具条组成，专业版三角洲泥作为最高的边界，和岸和浅湖泥或海藻的墩作为底部边界。他们垂直地被重叠并且水平地paralleled。形成水充满Cl−离子并且能与高咸度作为CaCl2类型被分类，它显示反常低压的分隔空间处于好封上的状况并且为油和煤气的累积和保藏有益。

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简介：BACKGROUND:ResearchesindicatethatpatientswithWilsondisease(WD)haveabnormalskeletalmetabolism,whichisinducedbyvariousfactors.OBJECTIVE:ToprobeintothechangingcharacteristicsofabnormalskeletalmetabolisminWDpatientsandobservetheeffectofdecoppertherapy.DESIGN:Case-contrastandself-controlstudy.SETTING:DepartmentofNeurology,AffiliatedHospitalofNeurologicalInstitute,AnhuiCollegeofTraditionalChineseMedicine.PARTICIPANTS:Atotalof35patientswithWDincluding21malesand14femalesagedfrom10to42yearswiththemeanageof(20±8)yearswereselectedfromDepartmentofNeurology,AffiliatedHospitalofNeurologicalInstitute,AnhuiCollegeofTraditionalChineseMedicinefromSeptember2000toFebruary2001.Allthepatientswereincompliancewiththediagnosticcriteria:historyoffamilyheredity;conesymptomsinvitro,physicalsignorliversymptoms;positiveKayser-Fleischerring;serumcopperprotein＜200mg/LorAcopperoxidase＜0.2;urinecopper＞1.6μmol/24hours;livercopper＞250μg/g(dryweight).Thecontrolgroupwasselectedfrom25casesofhealthindividualsincluding13malesand12femalesagedfrom16to35yearswiththemeanageof(22±6)years.Allpatientswhoparticipatedinthestudywereinformedfirstandconsented.METHODS:Patientsintreatmentgroupweretreatedwithvenousinjectionof1.0gsodiumdimercaptosulfonate,onceadayfortotally6successivedays.Andthen,patientsrestedfor2days.Thisprocedurementionedabovewasregardedasacourse,andthetreatmentlastedfor4-8courses.Beforeandafterinjectionofsodiumdimercaptosulfonate,serumcalcitonin(CT),osteocalcin(BGP),parathyroidhormone(PTH)and1,25-(OH)2VitD3weremeasuredwithradio-immunitymethod:blood,urinecalcium,phosphorumandurinecreatinineweremeasuredwithbiochemicalanalyzer;urinedihydropyrimidinedehydrogenase(DPD)wasdetectedwithenzyme-immunitymethod;bonemineraldensity(BMD)wascheckedattheonethirdfromdistalendofulnaandradiuswithsingle

简介：Weusedmatchedfilter,spectrumanalysis,andcontinuationmethodsofpotentialfieldfordataprocessingandobtainedthegeomagneticfielddistributionaboutthecontinentandcontinentalmargininsoutheastChina.Onthebasisofgriddata,inversionwasconductedandmagneticfielddistributionandmagneticstructureonbeddingofdifferentdepthswereobtained.Thenewresultsshowthat:1.ThemagneticfieldcharacteristicsarelargelydifferentinhorizontalandverticaldirectionsandtheycanbedividedintozonesaccordingtothecontinentalblocksofYangtze,Cathaysia,Kangdian(Sichuan-Yunnan)andQinling-Dabie.2.TheTanlufaultextendssouthwardalongtheGanjiangfaultandtheWuchuan-SihuifaultafteritcrossedovertheYangtzeRiverandwasoffsetlocallyintheeast-westdirection.TheTanlufaultfinallyslipsintotheSouthChinaSeaatHainanIsland.3.TheboundarybetweenYangtzeandCathaysiablocksstartsfromHangzhouBayintheeast,extendsalongJiangshaofaultandpassesthroughNanchang,Changsha,andGuilin,andfinallyenterstheseaatQinzhou,Guangxi.4.Thedistributionofburiedstructurezoneislocatedat24.5°-26°N.